A Challenging Case of IgG4-Related Disease with Multiple Relapses: Effective Treatment with Bendamustine and Rituximab

Immunoglobulin G4-Related Disease (IgG4-RD) is characterized by increased IgG4 serum concentrations, tissue infiltration by IgG4-secreting plasma cells, and fibrosis. Steroids and rituximab are effective has therapeutic agents for front line treatment.